L carnitine is primarily synthesized in the liver from the amino acids lysine and methionine through a series of four enzymatic reactions, with the liver and kidneys converting the precursor butyrobetaine into active Role of L carnitine in the transport of long chain fatty acids through Download Scientific Diagram The Role of l Carnitine in Mitochondria, Prevention of Metabolic Inflexibility and Disease Initiation Function of carnitine in the transport of mitochondrial long chain Download Scientific Diagram